Continuous and bimonthly publication
ISSN (on-line): 1806-3756

Licença Creative Commons
9957
Views
Back to summary
Open Access Peer-Reviewed
Relato de Caso

Respiratory bronchilitis-associated interstitial lung disease

Doença pulmonar intersticial associada a bronquiolite respiratória

Silvia CS. Rodrigues, Mauri M. Rodrigues, Ester MC Colleta, Nailê S Rocha, Carlos AC Pereira

ABSTRACT

Respiratory bronchiolitis-associated interstitial lung disease is one of many within the spectrum of smoking-related diffuse infiltrative lung diseases. The clinical and functional characteristics are typically subtle. Herein, we describe two cases of diagnosed through open-lung biopsy, and characterized by insidious evolution of dyspnea, digital clubbing, cystic lesions on computed tomography scans, and hipoxemia upon exertion. We emphasize that, when smokers are evaluated, it is imprtant to consider a diagnosis of respiratory bronchiolitis-associated interstitial lung disease in the context of interstitial cystitis, as well as in that of lymphangioleiomyomatosis, eosinophilic granuloma and idiophatic pulmonary fibrosis.

Keywords: Smoking. Interstitial lung diseases. Bronchiolitis.

RESUMO

A doença pulmonar intersticial associada a bronquiolite respiratória faz parte do espectro anatomopatológico das lesões pulmonares infiltrativas difusas induzidas pela fumaça de cigarro. Raramente tem apresentação clínicofuncional exuberante. Descrevemos dois casos diagnosticados por biópsia pulmonar aberta, caracterizados por dispnéia de evolução insidiosa, baqueteamento digital, lesões císticas à tomografia computadorizada e hipoxemia ao exercício. Enfatizamos considerar, em indivíduos tabagistas, a doença pulmonar intersticial associada a bronquiolite respiratória no contexto das pneumopatias intersticiais císticas, juntamente com a linfangioleiomiomatose, o granuloma eosinofílico e a fibrose pulmonar idiopática.

Palavras-chave: Tabagismo. Doenças pulmonares intersticiais.


THE CONTENT OF THIS ARTICLE IS NOT AVAILABLE FOR THIS LANGUAGE.


Indexes

Development by:

© All rights reserved 2024 - Jornal Brasileiro de Pneumologia